Phenylalanine hydroxylase

Found in the liver, this is an enzyme that catalyzes the conversion of ingested phenylalanine into tyrosine^[1].

A mutation in the human phenylalanine gene can result in the enzyme not being produced. This results in the condition phenylketonuria^[2].

References

1. ↑ Dutta,S.Goodsell, D. (2005) RCSB Protein Data Bank [1] Accessed 04/12/16
2. ↑ National Health Service (2014) [2] Accessed 04/12/16